Tag: pulmonary angiography

Cirrhosis of the Liver Simulating Congenital Cyanotic Heart Disease: Conclusion

Category: Heart Disease | Tags: arteriovenous fistulas, cyanotic heart disease, pulmonary, pulmonary angiography

In one of his two cases, Hales demonstrated pulmonary arteriovenous fistulas on postmortem injection of pulmonary vessels which could not be detected on pulmonary angiography or histology. Peripheral vein contrast echocardiography has been used to localize and quantitate intrapulmonary shunts. Normally, the echocardio-graphic contrast is completely eliminated in transit through the pulmonary capillary bed. In…

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Cirrhosis of the Liver Simulating Congenital Cyanotic Heart Disease: Pulmonary angiography

Cirrhosis of the Liver Simulating Congenital Cyanotic Heart Disease: Pulmonary angiography

Category: Heart Disease | Tags: arteriovenous fistulas, cyanotic heart disease, pulmonary, pulmonary angiography

The cause of desaturation of the arterial blood in cirrhosis has been investigated by some workers. The postulated mechanisms include portopulmonary venous shunting, shift of oxyhemoglobin dissociation curve, pulmonary diffusion defect, ventilation perfusion defect, and intrapulmonary shunting. The presence of anastomosis between portal and pulmonary veins via mediastinal veins has been demonstrated in some patients…

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Cirrhosis of the Liver Simulating Congenital Cyanotic Heart Disease: Discussion

Category: Heart Disease | Tags: arteriovenous fistulas, cyanotic heart disease, pulmonary, pulmonary angiography

Our group in 1966 reported seven patients suffering from cirrhosis of liver who showed severe cyanosis and gross clubbing and closely simulated congenital cyanotic heart disease. It was shown conclusively that cyanosis was secondary to intrapulmonary shunting through multiple tiny pulmonary arteriovenous fistulas. While with the advent of cross-sectional echocardiography it is easy to exclude…

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Cirrhosis of the Liver Simulating Congenital Cyanotic Heart Disease: Chest x-ray films

Cirrhosis of the Liver Simulating Congenital Cyanotic Heart Disease: Chest x-ray films

Category: Heart Disease | Tags: arteriovenous fistulas, cyanotic heart disease, pulmonary, pulmonary angiography

Intrasplenic pressure was measured in 12 cases where portal splenography was performed and was raised in all patients. Portopulmonary fistulas could not be demonstrated on portosplenography in any patient. In five cases, the portal vein could not be visualized and a few large colaterals were seen to open into the inferior vena cava. In the…

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Figure 1. Liver biopsy (case 1) showing irregular areas of fibrous tissue traversing the parenchymatous tissue, pseudolobulation, regenerating nodules. (From Hansoti RC, Shah RC. Cirrhosis of liver simulating congenital cyanotic heart disease. Circulation 1966; 33:71-7, by permission.)

Cirrhosis of the Liver Simulating Congenital Cyanotic Heart Disease: Results

Category: Heart Disease | Tags: arteriovenous fistulas, cyanotic heart disease, pulmonary, pulmonary angiography

The results of cardiac catheterization, angiography, and biopsy are shown in Table 1 and Figures 1 to 6. Eleven of the patients were men. All patients were between seven and 21 years of age. All of them showed severe cyanosis, gross clubbing, and grade 2-3 effort intolerance of one to six years’ duration. Eight patients…

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Cirrhosis of the Liver Simulating Congenital Cyanotic Heart Disease

Cirrhosis of the Liver Simulating Congenital Cyanotic Heart Disease

Category: Heart Disease | Tags: arteriovenous fistulas, cyanotic heart disease, pulmonary, pulmonary angiography

Central cyanosis in cirrhosis of liver was first described by Fluckiger in 1884, and subsequently, there have been a few stray reports describing desaturation of arterial blood in this condition. In 1966, Hansoti and Shah described a rare but distinct clinical entity in seven cases of cirrhosis of liver who presented with dyspnea, intense cyanosis,…

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